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1. Mayer AS, Stoller JK, Bucher Bartelson B, James Ruttenber A, Sandhaus RA, Newman LS.  Occupational exposure risks in individuals with PI*Z alpha (1)-antitrypsin deficiency.  Am J Respir Crit Care Med 2000, 162(2 Pt 1):553-8.

2. Strange C, Wilner I.  Alpha-1 Foundation Research Registry: from the past to the future.  J Ped Gastro and Nutrition 2002, 34:1.

3. Mullins CD, Wang J, Stoller JK.  Major components of the direct medical costs of alpha1-antitrypsin deficiency.  Chest 2003, 124(3):826-31.

4. Strange C, Dickson M, Carter C, Carpenter MJ, Holladay, Lundquist R, Brantly ML. Genetic testing for alpha1-antitrypsin deficiency. Genet Med 2004, 6: 204-10.

5. Fanos JH, Strange C. “The lion, the witch, and the wardrobe": impact of siblings of individuals with AAT deficiency. American J Medical Genetics 2004, 130(3):251-7.

6. Bowlus C, Strange C, Willner I, Reuben A, Xie L, Woolson R, Holladay B. Factors associated with advanced liver disease in adults with alpha1-antitrypsin deficiency. Clinical Gastroenterology and Hepatology 2005, 3(4):390-6. 

7. Strange C, Moseley MA, Jones Y, Schwarz L, Xie L, Brantly ML. Genetic testing of minors for alpha-1 antitrypsin deficiency, Arch Pediatr Adolesc Med 2006, 160:531-4.

8. Eden E, Holliday B, Xie L, Strange C. Asthma and allergy in alpha-1 antitrypsin deficiency. Respiratory Medicine, 2006; 100(8):1384-91.

9. Carpenter MJ, Strange C, Jones Y, Dickson MR, Carter C, Moseley MA, Gilbert GE. Does genetic testing result in behavioral health change? Changes in smoking behavior following testing for Alpha-1 Antitrypsin Deficiency. Ann Behav Med, 2007, 33(1):22-28.


1. Stocks JM, Brantly M, Barker A, Kueppers F, Strange C, Donohue JF, Sandhaus R. Multi-center study: the biochemical efficacy, safety and tolerability of a new alpha-1-proteinase inhibitor, Zemaira. Journal of COPD, 2006,3:17-23.

2. DeMeo DL, Sandhaus RA, Barker AF, Brantly ML, Edward Eden E, McElvaney NG, Rennard S, Burchard E, Stocks JM, Stoller JK, Strange C, Turino GM, Campbell EJ, Silverman EK. Determinants of airflow obstruction in severe alpha 1-antitrypsin deficiency. Thorax 2007,
62(9): 806-13.

3. DeMeo DL, Campbell EJ, Barker AF, Brantly ML, Edward Eden E, McElvaney NG, Rennard S, Sandhaus RA, Stocks JM, Stoller JK, Strange C, Turino GM, , Silverman EK. IL10 polymorphisms are associated with airflow obstruction in severe alpha 1-antitrypsin deficiency. Am J Respir Cell Mol Biol; 2008, 38:114-20.

4. Holm KE, Bowler RP, Make BJ, Wamboldt FS.  Family relationship quality is associated with psychological distress, dyspnea, and quality of life in COPD.  COPD, 2009 6(5):359-68.

Last updated: April 21, 2010


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